Pediatric Board Review Illustration Quiz 1

If you were to be presented with a picture of a child with dental abnormalities consistent with this picture, you are likely dealing with a child with Hallerman -Streiff Syndrome

What are the pathognomonic buzz words?

On the other hand you might be provided with a clinical vignette where this dental pattern is merely described as peg shaped, pointed and missing teeth and a smile that only a mother (can barely) love!

If you want to remember this association, just picture Hockey - Manwithout teeth instead of Hallerman

Hallerman - Streiff is a disease grouped under the ectodermal hypoplasia category.

In addition to dental abnormalities, the following may also be described or shown to you on the exam.

  • Hypoplastic nails
  • Fine Sparse hair
  • Abnormalities of the sweat and sebaceous glands
  • Short stature
  • Craniofacial abnormalties