Pediatrics Board Question/ Ectodermal Dysplasia

Pediatrics Board Question/ Ectodermal Dysplasia

Posted by Stuart C. Silverstein, MD, FAAP Author " Laughing Your Way to Passing the Pediatric Boards " ( R) on Oct 7th 2023

Pediatric Board Review  Question/ Ectodermal Dysplasia

On the ABP exam and Pediatric MOCA module you will be presented with images. May diseases and syndromes look similar and it is important to distinguish them quickly on the exam.  Here are two such examples and how to distinguish them easily ! 

The  image above  depicts the details of Ectodermal dysplasia which can be confused with Hallermann Streiff syndrome

Children with both ectodermal dysplasia and Hallermann Streiff can present with defective teeth, watch for the description or the details of the photo to tell them apart : 

Children with ectodermal hypoplasia have these 5 features :

• Peg teeth
• Pointed teeth / missing teeth
• Hypoplastic nails
• Fine sparse hair
• Abnormalities of sweat and sebaceous glands

Dentures is another common feature they may describe 

Children with Hallermann Streiff will be described as having  neonatal teeth

Click here for more information on Hallermann Streif syndrome 

Read our illustrated atlas which contains dozens of color and black and white illustrations including X-ray schematics. It focuses on the subtle differences between similar images and what to look for on the exam.

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