Pediatric Board Review : 5 Signs of Hallerman-Streiff
Posted by Stuart C. Silverstein, MD author Laughing Your Way to Passing the Pediatric Boards on Jan 22nd 2021
If you were to be presented with a picture of a child with dental abnormalities consistent with this picture, you are likely dealing with a child with Hallerman -Streiff Syndrome
What are the pathognomonic buzz words?
On the other hand you might be provided with a clinical vignette where this dental pattern is merely described as peg shaped, pointed and missing teeth and a smile that only a mother (can barely) love!
If you want to remember this association, just picture Hockey - Manwithout teeth instead of Hallerman
Hallerman - Streiff is a disease grouped under the ectodermal hypoplasia category.
In addition to dental abnormalities, the following may also be described or shown to you on the exam.
- Hypoplastic nails
- Fine Sparse hair
- Abnormalities of the sweat and sebaceous glands
- Short stature
- Craniofacial abnormalties